G ModelREVMED-6463:No.of Pages13ARTICLE IN PRESSLa Revue de medecine inteme xxx(xxxx)xxx-xxxDisponible en ligne surElsevier Masson FranceScienceDirectEMconsultewww.sciencedirect.comwww.em-consulte.comELSEVIERReviewFrench practical guidelines for the diagnosis and management ofrelapsing polychondritisProtocole national de diagnostic et de soins pour la polychondrite chroniqueatrophianteL.Arnaud a.*,N.Costedoat-Chalumeaub.c.d,A.Mathiane,L.Saillerf,A.Belot,J.Dionb.c.dN.Morelb.c.d,G.Moulisf,Collaborators,B.Bader-Meunierh,B.Bodaghii,A.Bura Rivierej,M.Casadevallk,O.Fain,C.Francesm,E.Hachulla,M.Hamidou,C.KarakoglouP,M.Lambert,F.Lerebours',G.Lerouxs,X.Mariette,C.H.Marquette",T.Martin,A.Mekinianw,T.Papox,J.-C.Piettey,X.Puechal2,C.Richez aa,A.Sarauxab,P.Sevec,F.Tankeread,.Terriouae,P.Varinafa Service de Rhumatologie,Hopitaux Universitaires de Strasbourg.Centre National de Reference des Maladies Auto-Immunes Est Sud-Ouest(RESO)Strasbourg FranceDepartment of Internal Medicine,Tle-de-France Rare Autoimmune and Systemic Diseases Reference Centre,hopital Cochin,Paris,FranceUniversity of Paris Cite,Paris,FranceInsem U1153,Centre de recherche en epidemiologie et statistiques Sorbonne Paris Cite(CRESS)Paris,Francee Service de medecine interne 2.Institut E3M.Inserm UMRS.Centre d'immunologie et des maladies infectieuses(CIMI-Parisgroupement hospitalierPitie-Salpetriere,Centre de reference du lupus syndrome des anticorps antiphospholipides et autres maladies auto-immunes rares,Assistancepublique-Hopitauxde Paris,Paris,FranceAbbreviations:Ab,antibodiesAFPCA,Association francophone contre la polychondrite chronique atrophianteANCA,anti-neutrophil cytoplasmic antibodyCBC,complete blood countCCP,citrullinated cyclic peptidesCOPD,chronic obstructive pulmonary diseaseCRI,Club Rhumatismes et InflammationCRP,C-reactive proteinCT.computed tomographyENA,soluble nudlear antigensENT,ear,nose and throatFPGDM,French Practical Guidelines for the Diagnosis and ManagementGPA,granulomatosis with polyangiitisGRIO,Osteoporosis Research and Information GroupHAS,French National Authority for HealthIBD,chronic inflammatory bowel diseasesIPSS-R,Revised International Prognostic Scoring SystemIV,intravenousLTC,long-term conditionMA,Marketing AuthorisationMAGIC,mouth and genital ulcers with inflamed cartilagesMPO.myeloperoxidaseMRL magnetic resonance imagingNSAID,non-steroidal anti-inflammatory drugPET,positron emission tomographyPFT.pulmonary function testingPR3,Proteinase 3SAVI,STING associated vasculopathy with onset in infancyTPE,therapeutic patient educationVEXAS,vacuoles,E1 enzyme,Xlinked,autoinflammatory,somaticWHO.World Health Organization.Corresponding author.Adresse e-mail:Laurentarnaud@chru-strasbourg.fr (L.Arnaud).https://doi.org/10.1016/j.revmed.2023.05.0050248-8663 2023 TheAuthors.Published by Elsevier Masson SAS on behalf of Societe Nationale Francaise de Medecine Interne(SNFMI).This is anopen access article underthe CC BY-NC-ND license(http://creativecommons.org/licenses/by-nc-
