有Check for updatesReceived:27 September 2022Accepted:16 January 2023D0L:10.1111/jdv.18931®JEADVGUIDELINESS2k guidelines on the management of paraneoplastic pemphigus/paraneoplastic autoimmune multiorgan syndrome initiated by theEuropean Academy of Dermatology and Venereology(EADV)Emiliano Antiga Rikke Bech2 Roberto Maglie Giovanni GenoveseLuca Borradori Barbara Bockles Marzia Caproni6 Frederic CauxNisha Suyien Chandran9 Alberto Corral Francesco D'Amorel0Maryam Daneshpazhooh Dipankar De2 Dario Didona3Marian Dmochowski4 Kossara Drenovska'5 Jan Ehrchen'6 Claudio FelicianiMatthias Goebeler Richard Groves9 Claudia Guinther0 Sanjeev Handa2Silke C.Hofmann22 Barbara Horvath23 Dimitrios Ioannidis Hana Jedlickova25Cezary Kowalewski26 Khalaf Kridin27,28 Pascal Joly29 Yen Loo Lim30,3Branka Marinovic3 Emanual Maverakis33 Joost Meijer23 Aikaterini Patsatsi3Carlo Pincelli35 Catherine Prost36 Jane Setterfield Eli Sprecher38,39Dusan Skiljevic4041 Kaisa Tasanen2 Soner Uzun3 Nina Van Beek4Snejina Vassileva15 Artem Vorobyev4 Igor Vujic4546 Gang Wang 7Mingyue Wangs49 Katarzyna Wozniak30 Savas Yayli Giovanna ZambrunoTakashi Hashimoto33 Enno Schmidt454 Jose Manuel Mascaro Jrs5Angelo Valerio Marzano36SectionofDermatology.Department of HealthSciences,University of Flrence.Florence.ItalyDepartment of Dermatology and Venerology.Aarhus University Hospital.Aarhus,DenmarkDermatologyUnit.Fondazione IRCCSCGranda Ospedale Maggiore Policlinico.Milan,ItalyDepartment of Dermatology.IntaBern University Hospital,University of Bern.Bern,SwitzerlandSDepartment of Dermatology.Venereology and Allergology.Innsbruck Medical University.Innsbruck.AustriaRare Diseases Unit,Azienda USLToscana Centro,European Reference Network Skin Member,Florence,ItalyDepartment of Dermatology.Groupe Hospitalier Paris-Seine-Saint-Denis.AP-HP,Bobigny.FranceDivision of Dermatology.Department of Medicine.National University Hospital Singapore,SingaporeDepartment of Medicine,NUS Yong Loo Lin School of Medicine.Singapore.SingaporeDepartment of Haematology.University Hospital of Aarhus.Aarhus,DenmarkDepartment of Dermatology.Autommune Bullous Diseases Research Center,Razi Hospital,University of MedicalSciences.Tehran.IranDepartment of Dermatology,PGIMER,Chandigarh.IndiaDepartment of Dermatologyand Allgology.Philipps University,Marburg.GermanyAutoimmune Blistering Dermatoses Section,Department of Dermatogy.Pznn University of Medical ScncesPozna Poland5Department of Dermatology and Venereology.Medical Faculty.Medical University.Sofia BuariaEmiliano Antigaand Rikke Bech shared first authorship.ose Manuel Mascar Jr and Angelo Valerio Marzano shared last authorship.This is anopen access article under the terms of the Creative Commons Attribution-NonCommercial License,which permitsuse,distributionand reproduction in anymedium,provided the original work is properly cited and is not used for commercial purposes.023The Authors.Journal ofthe European Academy of Dermatology and Venereology published by John Wily&Sons Ltdon beh